The lymphoproliferative auto-immune syndrome: a rare cause of peripheral cytopenia
نویسندگان
چکیده
منابع مشابه
Autoimmune lymphoproliferative syndrome (ALPS): a rare cause of immune cytopenia.
Autoimmune Lymphoproliferative syndrome (ALPS) is an inherited disorder manifesting with autoimmune cytopenia, lymphadenopathy and splenomegaly. The differential diagnosis includes infections, autoimmune disorders or malignancies. The disease is characterized by accumulation of double negative (CD3+ CD4- CD8-) T cells (DNT) in the peripheral blood. We describe a case and review the literature.
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ژورنال
عنوان ژورنال: Electronic Journal of General Medicine
سال: 2018
ISSN: 2516-3507
DOI: 10.29333/ejgm/94112